| Clinical description: This 9 year old female patient has a history of painless maxillary expansion for the past 5-6 years. She and her parents are interested in orthognathic surgery to correct the cosmetic defect. Her medical history is significant for a microcytic, hypochromic manemia. She has periodic blood transfusions to treat the anemia. She also has hepatosplenomegaly. Lateral skull radiographs show a “hair-on-end” appearance of the calvaria. | | | Radiographic findings: | | Postoperative radiograph: | |
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